Noncompaction cardiomyopathy, a frequently overlooked entity (…but beware of over diagnosis!)
نویسندگان
چکیده
منابع مشابه
Noncompaction cardiomyopathy is frequently associated with myopathy (left ventricular noncompaction with hypothyroidism and sensorineural hearing loss).
Ventricular myocardial “noncompaction” (MN), which is also called honeycomb or spongy myocardium, is a rare type of cardiomyopathy characterized by a hypertrophic left ventricle with deep trabeculations and poor systolic function, with or without associated left ventricle dilatation (1-3). It has been thought that the basic morphogenetic abnormality may be the arrest of normal compaction of the...
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Introduction: Noncompaction cardiomyopathy (NccM) is a rare form of cardiomyopathy. the American Heart Association classified it as a genetic cardiomyopathy. the pathogenesis of this condition is attributed to the failure of trabecular myocardium to compact and underdeveloped microcoronary circulation. case report: We present a case of a 72-year-old African American female who presented with sh...
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Pulmonary embolism (PE) is frequently a difficult diagnosis because of non-specific symptoms that can lead to misdiagnosis 1 . We report a patient with PE successfully diagnosed and treated, whose CXR showed Westermark’s sign of pulmonary embolism. Westermark’s sign is distal oligaemia in the affected area of the lung due to a reduction in size of vessels distal to a PE 2 . It has a low sensiti...
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Limitations in the Diagnosis of Noncompaction Cardiomyopathy by Echocardiography Viviane Tiemi Hotta,1,2 Sabrina Cunha Tendolo,2 Ana Clara Tude Rodrigues,3,4 Fábio Fernandes,2 Luciano Nastari,2 Charles Mady2 Instituto do Coração (InCor) do Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (HCFMUSP);1 Fleury Medicina e Saúde;2 Hospital das Clínicas – FMUSP;3 Hospital Is...
متن کاملNoncompaction cardiomyopathy: a current view.
Isolated non-compaction cardiomyopathy is a rare disease that is likely to develop in the embryonic period. It is caused by the intrauterine arrest of the myocardial compaction process in the beginning of the fetal development. It is characterized by prominent myocardial trabeculations and deep intertrabecular recesses, as well as the thickening of the myocardium into two distinct layers (compa...
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ژورنال
عنوان ژورنال: Netherlands Heart Journal
سال: 2012
ISSN: 1568-5888,1876-6250
DOI: 10.1007/s12471-012-0314-6